[A case of long QT syndrome].

نویسندگان

  • B A Bezkaravaĭnyĭ
  • S V Khripko
  • V M Bezkaravaĭnaia
چکیده

Introduction Long QT syndrome (LQTS) is a group of genetically distinct arrhythmogenic disorders resulting in abnormal cardiac sodium and potassium ion channels causing delayed repolarization of the heart. This syndrome can present clinically as syncope, seizures, or sudden cardiac death secondary to its characteristic ventricular arrhythmia of torsades de pointes. The clinical and electrocardiographic description of long QT syndrome was first reported in 1957 by Anton Jervell and Fred Lange Nielsen. Disease prevalence is estimated to be from 1 in 5, 000 to 1 in 20, 000. Schwartz et al proposed some major and minor

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عنوان ژورنال:
  • Pediatriia

دوره 8  شماره 

صفحات  -

تاریخ انتشار 1989